Non-Compaction Cardiomyopathy (NCC) (spongiform cardiomyopathy) is a rare congenital cardiomyopathy. NCC affects both children and adults. This is due to the failure of myocardial development during embryogenesis.Inthis casewepresenta 29years oldfemalepatient presenting with history of dyspnea on exertion and palpitation since 3 month duration. Echocardiography suggesting a biventricular non compaction associated with a Patent Ductus Arteriosus (PDA). Searching websites showed 8 case reports LV non-compaction associated with PDA in younger patients and this is the ninth case report of biventricular non compaction associated with PDA in an young patient.
Non-Compaction Cardiomyopathy (NCC) is a rare congenital cardiomyopathythat affects both children and adults.Itresultsfrom the failure of myocardial development. Prevalence of the disease is not known. NCC found in approximately 0.04%-0.05% of patients who underwent echo examination. NCC can present at any age. The clinical presentation of patientis highlyvariable. The incidence of complications and associated congenital heart diseases is high. Clinical presentation is non-specific and varies from no symptoms to conduction defect, thromboembolism, ventricular arrhythmias, severe heart failure, or sudden cardiac death[1-2].
A 29 years old female presented at our centre with progressive shortness of breath and palpitation since the past 3 month. Past historywas notsignificant. Patient was not on anymedications. She didn’t have any history of chest pain or syncope. At presentation patient had a pulse rate of, BP of 100/70 mmHg, pulse 110 bpm, SpO2 of 94% and signs of heart failure like elevated JVP, basal rales S3 and pedal edema. On examination there was short systolic murmur audible on left 2nd space area. ECG showed poor R wave progression. Chest X-ray suggested cardiomegaly. Echocardiography suggested four chamber dilatation (LVIDd-58 mm and LVIDs-48 mm) with severe LV dysfunction (LVEF 35%- 40%)
 

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